ISSN: 1300-0330 Dil: Türkçe, İngilizce
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Papillon - Lefevre Sendromu (olgu Raporu)
Prof.Dr. Nüzhet ARAS, Dr. Kerem BAYKAL, Doç.Dr. Ali Rıza GÜR, Dr. Tuncer ÖZEN
GATA Dermatoloji ABD, Diş Hekimliği Merkezi, ANKARA The syndrome of Keratosis palmoplantaris with periodontopathy
first described by Papillon and Lefevre in
1924, is a genetic disorder characterized by a symmetric
palmoplantar keratoderma and by a rapidly progressive
periodontopathy that leads to premature loss of both deciduous
and permanent teeth. The syndrome is inherited
as an autosomal recessive trait.
Here we present a Papillon-Levefre Syndrome case
as it is rarely seen.Keywords: Papillon-Lefevre syndromeT Klin Dermatoloji 1992, 2:155-158
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